Spielmeyer-Vogt disease is the juvenile form of a group of progressive neurological diseases known as neuronal ceroid lipofuscinoses (NCL). Also known as Speilmeyer-Vogt- Sjogren-Batten disease or Batten disease after a British pediatrician who first described it in 1903. Spielmeyer-Vogt disease is an autosomal recessive disorder. Therefore, when both parents carry the gene, their children have a 25% chance of developing the disease. Symptoms of Spielmeyer- Vogt disease are linked to the buildup of lipopigments in the body’s tissues. These lipopigments are made up of fats and proteins and build up in the cells of the brain and eyes as well as the skin, muscles, and other tissues.