Singleton-Merten syndrome is defined by Edward B. Singleton and David F. Merten (1973) as a syndrome of widened medullary cavities of the metacarpals and phalanges, aortic calcification and abnormal definition. It involves the unusual clinical features of abnormalities in, loss of, or absences of permanent teeth; calcium deposits on the aorta; and progressive diminution of bone density. The disorder appears to occur randomly, and its etiology is unknown. There is a possibility of autosomal dominant inheritance, which means that a single copy of the disease gene dominates the normal gene (The National Organization for Rare Disorders [NORD], 1997). Age of onset is between 4 and 24 months, and most cases reported a history of fever of unknown origin prior to onset.