Evans syndrome

An autoimmune disease characterized by thrombocytopenia and hemolytic anemia.


This refers to a rare autoimmune condition where the body mistakenly generates two antibodies – immune system proteins. One of these antibodies targets and attacks healthy red blood cells, and the other eliminates platelets, which are small cells in the blood crucial for clotting. Typically, the spleen is the primary location where these cells are destroyed.


The resulting anemia from this condition can lead to fatigue and a pale complexion, while the lack of platelets can result in bruising and a propensity to bleed readily. The process of hemolysis, which refers to the destruction of red blood cells, can cause jaundice, a condition marked by yellowing of the skin and the whites of the eyes.


During the initial stages of this condition, a blood transfusion might be required. To manage hemolysis and platelet destruction, corticosteroid medications could be recommended. In extreme instances, spleen removal may be necessary. Over time, spanning several months or years, the antibodies might eventually fade away.


 


Posted

in

by

Tags: