Also known as carnitine acyltransferase I or CAT1 is a mitochondrial enzyme, involved in converting long chain fatty acid into energy.
An essential enzyme crucial for the utilization of specific fats as an energy source is known as carnitine palmitoyltransferase (CPT). Inherited deficiency of this enzyme can result in exercise intolerance-induced rhabdomyolysis, a condition characterized by the breakdown of muscle fibers due to the inability to properly metabolize fats during physical exertion.