Klippel-trenaunay syndrome

Klippel-Trenaunay syndrome (KTS) is a congenital, vascular condition that usually affects the extremities. It also is known as angio-osteohypertrophy, nevus varicousus osteo- hypertrophicus syndrome, hemangiectasia hypertrophicans, and nevus verucosus hypertrophicans (Health Encyclopedia, 2001) and is commonly confused with several other similar conditions, including Klippel-Trenaunay- Weber syndrome, and Sturge-Weber syndrome. The most common characteristics of KTS is a port- wine stain on an extremity, although the literature does not agree with regard to which part of the body is most commonly affected. Although there is no clear agreement on the etiology of the disorder, it has been reasoned that the main characteristics of the syndrome are caused by diffuse capillary malformation near the surface of the skin.


 


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